Rare Tumors of the Neuroectodermal Origin: Report of Five Cases

نویسندگان

  • Vladimir Bauer
  • Zorica Aleric
  • Ervin Jancic
  • Tatjana Bujas
چکیده

We present a case series of five patients who were diagnosed in our institution with rare tumors of neuroectodermal origin. They were discovered within 1 year, by two otorhinolaryngologists at the county hospital which covers the area of about 1,00,000 inhabitants. Neuroectodermal tumors of the head and neck are rare pathologies, with extremely varied clinical behavior, treatment and prognosis. The lack of symptom specificity, the low incidence of these tumors and the difficulties associated with histopathology are main reasons for delayed diagnosis and treatment. We point out that rare tumors, if considered individually, have a low incidence, some even negligible, but the pathology detected hundreds of types which increases the likelihood that we will encounter some of them in our practice. Second, the practice in medicine does not always follow the statistical and mathematical probabilities but should take into account less possible occurrences.

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Peripheral Primitive Neuroectodermal Tumor of the Ovary: The Report of Two Rare Cases

Peripheral primitive neuroectodermal tumor (pPNET) is a highly aggressive small round cell tumor belonging to PNET/Ewing sarcoma family. Ovarian tumors composed of primitive neuroectodermal elements are extremely rare. Herein we reported two cases of peripheral primitive neuroectodermal tumors of ovary in two patients with different clinical presentations. Definite diagnoses were made bas...

متن کامل

Primitive Neuroectodermal Tumor (PNET) ofKidney -A Rare Entity

Primitive  neuroectodermal  tumor  (PNET)  of  kidney  is  an  extremely  rare  renal  neoplasm  with only about fifty reported cases in literature.  Presumably,of neural crest origin, these tumors behave  aggressively  and  carry  a  poor prognosis.  We  report  a  case  of  22-year  old  female  patient complaining of left loin pain with recurrent hematuria for last 3 months. On clinical ex...

متن کامل

Peripheral Primitive Neuroectodermal Tumor of the Pelvis

The primitive neuroectodermal tumor (PNET) belongs to a group of highly malignant tumors and is composed of small round cells of a neuroectodermal origin. Categorized in the same tumor family as Ewing sarcoma, the PNET is most likely to occur in bones and soft tissues. However, a small number of PNET cases arising in the pelvis have been reported as well. We present three cases of pelvic PNET: ...

متن کامل

Mandibular primitive neuroectodermal tumor in an adult dog

This is the report of a mandibular neuroectodermal/ewing sarcoma in an 8-year-old male cross breed dogthat is unique because of tumor origin location. Pedunculated, ulcerative, firm 6.0 × 4.0 × 5.5 cm tumor masseffaced the bone at the rostral part of the mandible and had a white-sanguineous color at cross sectionappearance. Histopathologically, small round blue cell tumor was diagnosed. Immunoh...

متن کامل

Bilateral Spontaneous Hemothorax with PNET: a case report and review

Background: Neuroectodermal Tumors (PNET) are malignant small cells neoplasm mainly occurring in children but can occur at any age. Extensive bleeding into the pleural cavity is rare In Children. Hemothorax would be compatible with a variety of congenital anomalies including sequestration, patent ductus artreiosus, and pulmonary arteriovenous malformation. Case report: A 2.5-years old girl who ...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

برای دانلود متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

عنوان ژورنال:

دوره   شماره 

صفحات  -

تاریخ انتشار 2012